Treatment of congenital generalized lymphangiectasia with propranolol in a preterm infant.
نویسندگان
چکیده
Generalized lymphangiectasia is a rare congenital disorder characterized by dilated lymphatic vessels with a fatal prognosis, especially in cases with thoracic involvement. We describe the use of propranolol in the therapy of generalized lymphangiectasia in a preterm infant with hydrops fetalis. Propranolol was well tolerated and effective within the first months. It remains to be shown whether propranolol is a treatment option for infants with generalized lymphangiectasia.
منابع مشابه
Treatment of Congenital Generalized Lymphangiectasia With Propranolol in a Preterm Infant abstract
Generalized lymphangiectasia is a rare congenital disorder characterized by dilated lymphatic vessels with a fatal prognosis, especially in cases with thoracic involvement. We describe the use of propranolol in the therapy of generalized lymphangiectasia in a preterm infant with hydrops fetalis. Propranolol was well tolerated and effective within the first months. It remains to be shown whether...
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ورودعنوان ژورنال:
- Pediatrics
دوره 133 2 شماره
صفحات -
تاریخ انتشار 2014